Globular glial tauopathy presenting as non-fluent/agrammatic variant primary progressive aphasia with chorea
نویسندگان
چکیده
منابع مشابه
Globular Glial Tauopathy Presenting as Semantic Variant Primary Progressive Aphasia.
Report of aCase |Theclinical, neuropsychometric, and imaging featuresof this casepreviouslywere reported in2008.2Briefly, awoman in her 60swas referred to the Behavioral Neurology Clinic formemory loss, characterizedbydifficulty rememberingnames.Longitudinal evaluations revealedprogressiveanomia with loss of word knowledge, prosopagnosia, and surface dyslexia. Her last completed neuropsychometr...
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Frontotemporal dementia (FTD) is a clinically and pathologically heterogeneous neurodegenerative disorder associated with atrophy of the frontal and temporal lobes. Most patients with focal temporal lobe atrophy present with either the semantic dementia subtype of FTD or the behavioral variant subtype. For patients with temporal variant FTD, the most common cause found on post-mortem examinatio...
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The non-fluent/agrammatic variant of primary progressive aphasia (naPPA) is a young-onset neurodegenerative disorder characterised by poor grammatical comprehension and expression and a disorder of speech sound production. In an era of disease-modifying treatments, the identification of naPPA might be an important step in establishing a specific cause of neurodegenerative disease. However, diff...
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OBJECTIVE To report the clinical, neuropsychological, linguistic, imaging, and neuropathological features of a unique case of sporadic Jakob-Creutzfeldt disease in which the patient presented with a logopenic variant of primary progressive aphasia. DESIGN Case report. SETTING Large referral center for atypical memory and aging disorders, particularly Jakob-Creutzfeldt disease. PATIENT Pat...
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A 66-year-old woman presented with 4 years of progressive speech difficulty. She had nonfluent speech with phonemic errors but intact single-word comprehension and object knowledge. Her grammar was impaired in both speech and writing, and she exhibited orofacial apraxia. A clinico-radiologic (see figure) diagnosis of nonfluent variant primary progressive aphasia was made. Nonfluent variant prim...
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ژورنال
عنوان ژورنال: Parkinsonism & Related Disorders
سال: 2017
ISSN: 1353-8020
DOI: 10.1016/j.parkreldis.2017.09.006